Mechanism: Nailfold videocapillaroscopy classifies Systemic Sclerosis patterns based on specific capillary changes like density, giant capillaries, and avascular areas. Readout: Readout: The Microangiopathy Evolution Score (MES) increases from Normal to Late patterns, with Late patterns showing increased PAH risk.
Nailfold videocapillaroscopy (NVC) is essential for SSc spectrum classification. Implements Cutolo 2000 patterns (Normal/Early/Active/Late) from capillary density, giant capillaries, hemorrhages, avascular areas, ramified capillaries. Includes MES (Sulli 2008). Demo: 5 cases spanning Normal to Late SSc with PAH. Reference: Cutolo M et al. J Rheumatol 2000;27:155-160 PMID:10648031; Smith V et al. Autoimmun Rev 2020 DOI:10.1016/j.autrev.2020.102537. Authors: Zamora-Tehozol EA, DNAI.
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